Anomalous origin of one pulmonary artery from the ascending aorta is a rare congenital malformation. It happens as the result of abnormal development of the 6th aortic arch. Anomalous origin of right pulmnary artery is more frequent than left. It is frequently associated with P.D.A., V.S.D. and T.O.F. In this malformation, congestive heart failure develops in early life and once the... |
Idiopathic Hypertrophic Subaortic Stenosis is a primary disease of cardiac muscle that is probably congenital, is often genetically transmitted, and is characterized by asymmetric septal hypertrophy, systolic anterior motion of anterior mitral valve and disorganization of cardiac muscle cells. The authors experienced 3 cases of Idiopathic Hypertrophic Subaortic Stenosis which were confirmed by echocardiography, cardiac catheterization and angiocardiography. The literatures... |
Among the double outlet right ventricle, S.D.L. type with subpulmonic ventricular septal defect is extremely rare. We experienced 10 year old girl who had S.D.L. type of double outlet right ventricle with subpulmonic mitral valvular insufficiency and LV-RA canal. The literature were reviewed. |
Twenty four cases of acute lymphocytic leukemia with mediastinal mass were studied at the Department of Pediatrics, Seoul National University Hospital from September 1965 to August 1983. Analysis were done with regard, to age, sex, chief complaints, organ size (liver, spleen and lymph nodes), initial hemoglobin, white blood cell and platelet count, initial bone marrow findings and lymphoblast surface markers.... |
Papaillary thyroid cancer is a rare lesion in children. It progresses slowly and its prognosis is relatively good. A painless nodule in the thyroid or in the neck is the usual first evidence of disease. Cervical lymph node involvement is usually present at the time of the initial diagnosis and is often bilateral. The lungs are the most common site... |
The anomalous origin of the left coronary from the pulmonary artery is a rare congenital cardiac anomaly and there has been no case reported in Korea. We report one case of the anomalous origin of the left coronary artery from the pulmonary artery. He was an 11 month-old male body, who was suffered from congestive heart failure since 5 months of... |
Supravalvular stenotic ring of the left atrium is one of the rare anomalies, which is usually accompanied by other cardiac defects. It is very important to recognize its existence earlier and preoperatively. Main tools in. diagnosis are angiocardiography and echocardiography. We have experienced a patient with supravalvular stenotic ring of the left atrium with coexisted with VSD and PDA. M-mode... |
Twenty-nine cases of Kawasaki disease, who were admitted to the Dept, of Pediatrics, Seoul National University Hospital, were evaluated on the incidence, clinical signs and laboratory findings of cardiovascular system. Among them two patients were excluded from the incidence of cardiac involvement: One with incomplete study died at home on 22nd day after the onset, and the other was referred because... |
Forty five cases of dilated cardiomyopathy who were admitted, to Seoul National University Hospital from June, 1980 to May, 1983 were studied on the clinical features and laboratory findings. 1) Twenty two cases (44.4%) were primary dilated cardiomyopathy, and the other 25 case (55.6%) were secondary. Nineteen cas&s(95.0%) of primary dilated cardiomyopathy were diagnosed within 3 year of age, but sacondary dilated cardiomyopathy did... |
Cor triatriatum is a rare congenital cardiac anomaly in which the left atrium is divided into two chambers by an abnormal fibro-muscular septum with, a small opening or not, product pulmonary venous obstruction and pulmonary hypertension. Three cases of cor triatriatum were observed at the Dept, of Pediatrics, Seoul National University. Each patient had no specific problem during early infancy, and presented... |
Transient myeloproliferative disorder has been reported in infants with Down syndrome. Infants with Down syndrome and this transient myeloproliferative disorder often present with signs and symptoms that are clinically and hematologically indistinguishable from congenital acute myelogenous leukemia. In contrast to congenital AML, complete clinical and hematological recovery occurs within weeks to months of diagnosis without any specific anti- leukemic treatment. A case of transient myeloproliferative disorder... |
Out of 1617 cases of congenital heart disease, who were admitted to the Pediatric ward, Seoul National University Hospital, for cardiac catheterization during recent 5 years, 20 patients with anomalous inferior vena cava were observed. Associated cardiac and extracardiac vascular anomalies were reviewed. Cardiac and visceral malposition were also analyzed. Results; 1) Incidence was 1.2% of total 1617 catheterized patients. 2) Male and female... |
Twenty one cases of triciispid atresia which were diagnosed at the department of Pediatrics, Seoul National University Hospital during past twelve years and eleven months were reviewed and analysed. The results were as follows. 1) There were 8 males and 13 females. According to anatomical classification, 15 cases were in type 1, 4 cases in type 표 and 2 cases in type... |
Supracristal ventricular septal defect has engendered an interest in recent years because of the racial difference in its incidence and the unusually high association of the aortic valve abnormalities. The relative incidence of supracristal ventricular septal defect was studied in Korean. During the period of eight years from January 1974 to December 1981, 119 cases(27.6%) of supracristal type were noted among 431 cases of... |
Five hundred and thirty-nine cases of malignant tumors (excluding leukemia) under 15 years of age who were admitted to Seoul National University Hospital from January 1967 to December 1981 were reviewed and analysed. Three hundred and ninety-nine cases of leukemia were seen during the same period and total 938 cases of malignancies including leukemia were observed. 1. The frequency of malignant tumors... |
Kostmann syndrome (Infantile genetic agranulocytosis), a disease characterized by recurrent infections leading to death in infancy, shows an agranulocytosis with variable monocytosis, eosinophilia in the peripheral blood, accompanied by the maturation arrest of the myelocytic series at the promyelocyte-myelocyte level. A 2 years 3 month old female patient with Kostmann syndrome is reported, who has suffered from recurrent infections since 1 month of age. During... |
Pericarditis denotes worse prognosis in patients with rheumatic fever. During the period of 4 years from Jan. 1978 to Dec. 1981, one hundred and eighteen patients were diagnosed as rheumatic fever on the basis of revised Jones* criteria. One hundred and one patients of them were evaluated with M-mode echocardiography, and were analysed according to Horo- witz^ classification of pericardial effusion. The results were as... |
Total anomalous pulmonary venous connection (TAPVC) is a rare congenital defect in which all the pulmonary veins are connected to the right atrium or its tributary veins. Without surgical intervention, most patients with TAP VC have grave prognosis, with cardiac failure and death in infancy. But owing to the advances of surgical technique and postoperative care, complete correction has been accomplished with good results. Sixteen... |
1. A total of 3,178 strains of Staphylococcus aureus, 278 strains of Shegella and 506 strains of Salmonella were isolated and tested for sensitivity against antimicrobial agents at Seoul National University Hospital from January 1971 to December 1980. Clinical study was made on children under 15 years old. 2. Sensitive strains to antimicrobial agents were more frequently isolated in children than adult. But the pa竹ern of sensitivity... |
Eighteen cases of double outlet right ventricle were observed during past six years at the department of pediatrics, Seoul National University Hospital. 1. Therw were 13males and 5 females. Sex ratio showed male predominance with the ratio of 2, 6:1. 2. According to the Sondheimer's classification, 6 cases were in group l, none in group ll, 10cases in group lll... |
Pulmonary artery aneurysms are extremely rate and are seldom diagnosed during life. In true aneurysms, dilatation tends to be confined to the main trunk of the artery and degenerative changes in the wall are found. In 1971, Williams et al reported the first successful excision and replacement of the main pulmonary artery, including the bifurcation, with a dacron graft. Since... |
Leukemic infiltration of the testes has been relatively rare disease. But increased survival due to advance in the treatment of childhood leukemia has been associated with an increase in incidence of leukemic infiltration of the tests. Six of 66 male children with acute lymphocytic leukemia and 2 of 2 male children with leukemic transformation on non-Hodgkin's lymphoma, who have been... |
Sixty two properly treated acute lymphocytic leukemia cases who were diagnosed at SNUH, from 1958 to July, 1981 were studied. Among them, 20 cases had survived more than 3 years and 42 cases survived less than 3 years. The 11 cases of 20 are now alive and off theray and the remainder 9 cases were expired after survival for more... |
Histiocytic Medullary Reticulosis(H.M.R.) is a rapidly progressing fatal disease seen most often in adults, but it has been reported in children younger than 15 years of age. H.M.R. is clinically characterized by fever, wasting generalized lymphadenopathy and hepatosplenomegaly. In the terminal stage, jaundice, purpura, anemia and pancytopenia are all present with or without skin involvement. Cardinal pathologic features are systemized... |
The effect of lithium carbonate was investigated on the five cases of aplastic anemia with measuring of serum level and EKG check. Reticulocyte count increased slightly only in one case. Hemoglobin, WBC and platelet count did not show any significant increase in all cases. No apparent side effect, including EKG finding, was observed. |
Five cases of Fanconi anemia were observed during these 7 *years. It acounts for about 6.7% of the total 75 aplastic anemia seen during those same period in SNUH. Three were boys and two were girls. The initial symptom was nasal bleeding or pallor which observed between the age of 2 years and 6 years. They all revealed growth retardation... |
Right atrial myxoma is a rare primay intra cardiac tumor and it presents various clinical manifestations mimicking Tricuspid stenosis, Constricive Pericarditis, and Subacute Bacte rial Endocarditis A 10 years old boy with exertioal dysyonea and general weakness for 40days was admitted to our hospital under the impressionof right atrial myxoma.clincal diagnosis was made by echocardiogram, cardiac catheterization and right artiograhpy... |
Replacement of cardiac valves in the pediatric patients is infrequent compared with in adult for the treatment of diseased heart valve. Furthermore, uncertainties regarding the long term fate of prosthetic value and effects of a fixed-orifice walve in the growing children are the main concern in pedriatric patients. Between January 1974 and October 1979, in 10 children, 15years or younger,... |
Pre-adoption screening examination was performed on 1257 infants and children. Routine physical examination and laboratary examination(urinalysis, blood examination, Tb skin test, VDRL, PKU and chest X-ray on children older than 2 years of age) were done. Further laboratory examinations were performen on the children with abnormal findings by the first screening. The results were as following. 1. Sex: Girls were... |
In spite of prevalence of diphtheria, there were scant reports about immunity to diphtheria Korea. The Schick tests were done in the admitted patients to the pediatric department of the SUNH and in the children at the Bupyung area. Among the total children, 22.5% were Schick-positive. The positive rate of the patients of SUNH is 19.7%, which is different form... |