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Case Report
A Case of Pseudo-Bartter's Syndrome Due to Hypertrophic Pyloric Stenosis
Yoon Hee Kim, Yoon Hee Kim, Tae Ho Lee, Tae Ho Lee, Hong Bae Kim, Hong Bae Kim
Clin Exp Pediatr. 2002;45(11):1430-1434.   Published online November 15, 2002
We report a 3-month old boy admitted to our hospital with Bartter's syndrome like symptoms and laboratory findings, which were vomiting, failure to thrive, hypochloremic and hypokalemic metabolic alkalosis associated with hyperreninemia, hyperaldosteronism and normal blood pressure. However, the urine chloride level was low. Hypertrophic pyloric stenosis was diagnosed through abdominal ultrasonography. Fredet-Ramstedt operation was done after electrolyte correction. After...
A Case of the Use of Intravenous Immunoglobulin of Treatment for HyperIgE Syndrome
Yoon Ji Choi, Dong IL Lee, Hong Bae Kim
Clin Exp Pediatr. 2001;44(11):1301-1304.   Published online November 15, 2001
Hyper-IgE syndrome is a rare congenital immune deficiency disease characterized by severe eczema, recurrent infection of the sinopulmonary tract, cold subcutaneous abscess and high serum IgE levels. It is an autosomal dominant disease with incomplete penetrance. We examined the case of a 12 month old infant with hyperIgE syndrome since neonate. The diagnosis of hyper IgE syndrome was made because...
A Case of Congenital Long QT Syndrome with Reccurent Syncope
Jong Hwa Hwang, Hong Bae Kim
Clin Exp Pediatr. 2000;43(5):725-729.   Published online May 15, 2000
Congenital long QT syndrome(LQTS) is a disease characterized by prolongation of ventricle repolarization and by the occurrence, usually during emotional or physical stress, of life-threatening arrhythmias that lead to sudden death in most symptomatic and untreated patients. Two variants have been initially identified : the original Jervell and Lange-Nielsen syndrome of congenital deafness and autosomal recessive inheritance, and the more...
A Case of Epstein's Syndrome
Seon Young Choi, Hyun Chul Chae, Hae Young Cho, Hong Bae Kim, Ji Sub Oh
Clin Exp Pediatr. 1994;37(11):1610-1614.   Published online November 15, 1994
Epstein's syndrome is a rare disease whish is characterized by the association of thrombocytopenia, macrothrombocytopathia, nephritis and deafness. We experienced a case of Epstein's syndrome in a 12 years old male patient who was presented with a life long history of bleeding, usually as epistaxis, bilateral sensorineural deafness and hematuria with proteinuria starting in the childhood. Hematologic studies showed thrombocytopenia with...
Original Article
Effect of Cyclosporin, Indomethacin and Methylprednisolone on Puromycin-Aminonucleoside Induced Nephrosis in Rats
Hong Bae Kim, Hae Lee Chung, Cheol Woo Ko, Ja Hoon Ko, Jung Sik Gwak
Clin Exp Pediatr. 1993;36(4):495-505.   Published online April 15, 1993
This experimental study was conducted to evaluate the effect of indomethacin and methylprednisolone on PAN-induced nephrosis in rats. Sprague-Dawley rats weighing 150∼200gm were used and divided into controls, group Ⅰ(PAN intraperitoneally), group Ⅱ(PAN intraperitoneally, followed by indomethacin peritoneally for 12 days), group Ⅲ(PAN intraperitoneally, followed by methylprednisolone peritoneally for 12 days) and group Ⅳ(PAN intraperitoneally, followed by cyclosporin subcutaneously for...
Case Report
A Case of Pseudohypoaldosteronism
Yong Soon Kwon, Hyo Gyoung Shin, Mi Soo Ahn, Hong Bae Kim
Clin Exp Pediatr. 1992;35(7):984-988.   Published online July 15, 1992
Pseudohypoaldosteronism(PHA) is rare salt losing disease which is characterized by mineralcorticoid unresponsiveness of the end organ. Severe hyponatremia and hyperkalemia are present despite high plasma aldosterone. We experienced a case of PHA in a 40-days old male infant who was presented with anorexia, vomiting and lethargy for several days. Labortory data showed hyponatremia, hyperkalemia and metabolic acidosis. Renal function was normal...
Original Article
The clinical study on MCLS.
Young Sun Ko, Ji Sun Cho, Hong Bae Kim, Ji Sub Oh
Clin Exp Pediatr. 1991;34(2):240-249.   Published online February 28, 1991
Forty six children with mucocutaneous lymph node syndrome were diagnosed and treated through admission at the Department of Pediatrics, Wallace Memorial Baptist Hospital from January 1987 to January 1990. Ther were investigated for clinical pattern and laboratory correlations. The results were as follows: 1) Most patients (95.7%) were under four years of the age. 2) The ratio of male to female was 1.6:1. 3) Seasonal incidence was high in...
A Case of Adrenal Cortical Carcinoma.
Ho Won Kang, Hong Ja Kang, Hong Bae Kim, Ji Sub Oh
Clin Exp Pediatr. 1990;33(8):1159-1165.   Published online August 31, 1990
This is a case report of adrenal cortical carcinoma in a 2 year 7 month old male patient who was diagnosed by clinical features, endocrinologic studies, radiologic studies and pathologic examina- tions. Cushing syndrome and virilization caused by adrenal cortical carcinoma were found. Left total adrenalectomy was performed. No evidence of metastasis was found at the time of operation. 3 months later, lung metastases...
Clinical Studies of Urinary Tract Infection in Infant and Children.
Kee Sung Yang, Mi Soo Ahn, Hong Bae Kim, Ji Sub Oh
Clin Exp Pediatr. 1989;32(4):533-541.   Published online April 30, 1989
Clinical studies on the 82 patients of sympomatic urinary tract infection who were admitted to pediatric department of Wallace Memorial Baptist Hospital from August 1984 to July 1987 were subjected in this study. The result were as follows. 1) The incidence was 0.79% of total pediatric inpatients during the same period. 2) Age incidence disclosed under 1 year in 49 patients(59.7%) and under 6 year...
A Case of Adrenoleukodystrophy.
Kee Sung Yang, Soo Tack Bae, Hong Bae Kim, Ji Sub Oh
Clin Exp Pediatr. 1989;32(3):430-437.   Published online March 31, 1989
We experienced a case of Adrenoleukodystrophy (ALD), which is a genetically determined metabolic disorder associated with progressive demyelination of brain white matter and adrenal insuficiency. An 11 year old male revealed rapidly evolving neuologic progression, decreased adrenal reserve, increased plasma content of very long chain fatty acids (VLCFAs) and typical radiological findings. We report here the clinical findings of this patient with brief review of...
Clinical Study of Patients with Mycoplasma Pneumoniae Pneumonia in Children.
Kyun Woo Lee, Young Ok Seo, Hong Bae Kim, Ji Sub Oh
Clin Exp Pediatr. 1988;31(2):167-176.   Published online February 28, 1988
Meconium Staining; A Five Year Retrospective Review.
Kei Hag Son, Kyun Woo Lee, Hong Bae Kim, Soom Ok Byun, Ji Sub Oh
Clin Exp Pediatr. 1987;30(1):26-34.   Published online January 31, 1987
Among a total of 15,250 newborns delivered at wallace memorial Baptist Hospital in a 5 year period from January 1980 to December 1984, a clinical study was done regarding meconium stained babies. The results were summarized as follows; 1) The incidence of meconium staining was 10.94% (1,669 babies). 2) Most of the meconium group (95.08%) had a birth weight exceeding 2,500 grams. The incidence of meconium staining...
Case Report
A Case of Congenital Giant Hydronephrosis.
Un Ki Yoon, Young Ok Seo, Hong Bae Kim, Ji Sub Oh, Ok Ji Paik
Clin Exp Pediatr. 1986;29(11):1251-1256.   Published online November 30, 1986
We would like to report an experience with a case of Giant Hydronephrosis due to Congenital left ureteropelvic junction obstruction in a 7 year-old boy who presented with palpable abdominal mass. The diagnosis was made through intravenous pyelogram, ultrasonogram and abdominal computerized axial tomogram. A brief review of the related literature is given.
Original Article
Diagnostric Significance of Subxiphoid Two-Dimensional Echocardiography in Congenital Heart Desease of Chlidred.
Kwang Do Lee, Cheol Woo Ko, Hong Bae Kim, Sang Bum Lee, Doo Hong Ahn
Clin Exp Pediatr. 1986;29(3):296-304.   Published online March 31, 1986
Subxiphoid, two-dimensional echocardiographic examinations were performed and interpreted before diagnostic cardiac catheterization on 138 patients with suspected congenital heart disease who were from 2 months to 15 years old. Cardiac catheterization and cineangiographic examination were performed in all patients and surgery in 99 patients and comparisions were made with each other. Eighteen of nineteen patients with an atrial...