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Since the effect of phototherapy in the treatment of neonatal hyperbilirubinemia has been reported 30 years ago, phototherapy has been used widely for neonatal hyperbilirubinemia, but the exact mechanism and the effect of light on the human body have not been fully determined. Free bilirubin level in the serum is an important indicator for kemicterus, a complication of neonatal hyperbilirubinemia. Free bilirubin level was... |
The authors studied 75 cases of congenital syphilis in the newborn treated at II Sin Christian Hospital from January 1983 to December 1987. The results were as follows; 1) The incidence of syphilis among the admitted pregnant women for delivery was 0.62%. 2) The incidence of neonatal syphilis from the 208 syphilis mothers was 36.1%. 3) The incidence of prematurity and low birth weight neonate among congenital syphilitic... |
In order to estimate the influence of systemic hemodynamic change in cerebral blood flow before and after closure of ductus arteriosus in premature mewborn infants, blood flow velocities of internal carotid artery (ICA), anterior cerebral artery (ACA) and middle cerebral artery (MCA) were measured in 17 premature newborn infants by pulsed Doppler ultrasonography. The data was compared with those of normal full-term infants by... |
34 very low birth weight infants weighing 1,500 gms or less, who were admitted to the neonatal intensive care unit of Seoul National University Children’s Hospital, were routinely studied with serial real-time brain ultrasonography from August 1, 1986 to July 31, 1988. Their medical records and the results of brain ultrasonography were analyzed to evaluate propor- tion, severity, timing, clinical findings, outcome, associated periventricular... |
Two dimensional echocardiographic examinations of the proximal left and right coronary artery were performed in 140 infants and children without heart disease. Eighty boys and 60 girls were studied whose ages ranged from newborn to 15 years old. The diameter of the proximal left cornonary artery was 0.8 mm in newborn and 1.9 mm in teenagers. The diameter of the proximal right coronary artery... |
29 patients admitted into Department of Pediatrics, Severance Hospital, Yonsei University, college of medicine during 16 years period from 1974 to 1989 with the diagnosis of fulminant hepatic failure were divided into 2 groups, live and expired groups. These patients were compared with sex, age distribution and etiology and in order to find the factors responsible for death platelet counts, prothrombin time, SGOT, SGPT,... |
To study the relationship between large amount of whole cow’s milk (WCM) intake and iron deficiency anemia (IDA) in early childhood, we carried out the study on 9 children with IDA, who were fed WCM, about 1,000 ml over 3 months, experienced at the department of Pediatrics, Seoul National University Hospital, during 5 months from March 1989 to July 1989. The results were as... |
Out of a total of 140 children hospitalized with the diagnosis of Kawasaki disease at the Depart- ment of Pediatrics, Hanyang University Hospital during the period of 9 years from July 1980 to July 1989, 68 cases were subjected to echcocardiographic examination at 10 to 15 days after the onset of illness, and these 68 cases were divided into two groups according the... |
Clinical features and endocrine function of 3 children with isolated TRH deficient congenital hypothyroidism followed at Seoul National University Children’s Hospital from Aug, 1986 to Aug. 1990 were reviewed. During above period 262 congenital hypothyroid patients were followed at endocrine clinic, number of congenital primary hypothyroidism was 218 cases (83.2%), and that of congenital secondary hypothyroidism was 44 cases (16.8%). Of the congenital primary hypothyroidism,... |
It has been known that intrauterine thyroid hormone deficiency may be one of the factors predis- posing to RDS in premature infants. L-thyroxine has been shown to increase the production opf lung surfactant, widely accepted as deficient in RDS infants, as association between lung immaturity and fetal thyroid function is postulated. The authors investigated thyroid hormone concentration at birth and 5, 15 days of... |
Hypertrophic cardiomyopathy is a common genetically transmitted disorder characterized by asymmetric septal hypertrophy and systolic anterior motion of the mitral valve. We have recently experienced identical twin with the hypertrophic cardiomyopathy confirmed by M-mode and 2-D echocardiography. It is the first report of hypertrophic cardiomyopathy in identical twin in Korea. So presented this case with a review of referential literatures. |
Esophageal variceal bleeding is a rare manifestation in childhood and it usually occurs secondary to portal hypertension. We experienced a case of esophageal variceal bleeding secondary to portal hypertension associated with portal obstruction but with no evidence of liver cirrhosis in a 4-year- and-10-month-old boy who was hospitalized due to hematemesis. He was a product of fullterm normal spontaneous delivery at home unattended by... |
Neuronal migrational disorders of the brain represent abnormalities in the formation of the neocortex caused by faulty migration of the subependimal neuroblasts. Lissencephaly is a rare congenital anomaly representing an arrest of brain development before the third or fourth month of gestaional age. The most common clinical findings were seizure, delayed development, failure to thrive and hydrocephalus. The authors experienced a case of lissencephaly with... |
Transverse myelopathy is characterized by a sudden onset of motor weakness and sensory loss on the distribution under the affected spinal cord level. And slso, autonomic nerve functions may be disturbed at the same time. The etiology is still unknown. But it is thought that numerous conditions and diseases are associat- ed with it. We experienced 3 cases of transverse myelopathy preceded by Korean hemorrhagic... |
Encephaloele which generally denotes a cephalic hernia through a congenital defect in the skull is relatively frequent congenital malformation whose incidence has been estimated at one in every 3,000 to 10,000 live births. The great majority of encephaloceles are located in the occipital area. Three- quarters of the childen with occipital encephaloceles are females. We have experienced a one day old girl who had... |
Arthrogryposis Multiplex Congenita is a very rare disease of persistent joint abnormalities present at birth. We experienced a case of arthrogryposis multiplex congenita in identical twin, and a review of literature was made. |
We experienced a case of hereditary spherocytosis patient who was in a recovery phase of aplastic crisis at the time of presentation. This was a 7 years old boy with complaints of pallor and intermit- tent abdominal pain. Asymptomatic jaundice was also found in the patient's grandfather and two maternal uncles. Patient’s mother had splenectomy due to hereditary spherocytosis. Diagnosis was made by morphology,... |
Acute megakaryoblastic leukemia is an uncommonly recognized disorder that is characterized by rapidly progressive proliferation of atypical megakaryocytes and their precursor cells, and fatal course. Abnormalities in chromosome 21 may have more than relationship to it. The authors report a case of acute megakaryoblastic leukemia in a 17 day-old male patient who was admitted for evaluation of high fever and dyspnea. The infiltration of atypical megakaryocytes... |
Pulmonary blastoma is a rare primary lung tumor consisting of a mixture of blastomatous and immature-looking epithelial and mesenchymal components. The histogenesis is not clarified. This disease is first described by Barnard in 1952 as “embryoma of lung” because of its resemblance to fetal lungs. In 1961, Spencer reported three new cases and suggested the name ^pulmonary blastoma” because of the resemblance to nephroblastoma... |
A 12 year old girl suffering visual disturbance for 4 months, and polydipsia and polyuria for last 20 days revealed an ovoid homogeneous mass on enhanced sella turcica coronal CT scan and result of water deprivation test was compatible with that of diabetes insipidus. Subtotoal rescetion of the brownish soft mass (0.5 x 0.7 cm) of pituitary stalk was performed neurosurgically, and histologically the... |