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The studies were carried out to analyze the emergency patient visited to the emergency room of the National Medical Center under the 15 years old during the three-year period from Jan., 1985. to Dec., 1987 The results were obtained as below. 1) During the 3-year periods, the total number of emergency patients under the 15 years of age was 4,394. 2) Forty one percents of the total patient... |
Idiopathic respiratory distress syndrome (IRDS) of the newborn remains an important and signifi- cant cause of morbidity and mortality despite of improvement in neonatal care. The clinical and radiologic features observed are the results of surfactant deficiency combined with a highly compliant chest wall. We have been applied the clinical and radiologic features in the diagnosis of IRDS. In 1974, Bomsel et al reported the... |
Among a total of 667 newborns delivered at Han Gang Sacred Heart Hospital from January 1988 to July 1989, a clinical study was done regarding meconium-stained babies. The results were summarized as follows: 1) The incidence of meconium staining was 25.9% (173 babies) and there was no difference of frequency in sex. 2) The higher the birth weigt and the gestational age, the higher the incidence of... |
A clinical study on the effects of exchange transfusion on disseminated intravascular coagulation was conducted on 32 patients with DIC who were admitted to the pediatric department of YUMC from January 1984 to June 1989. We diagnosed DIC when symptoms were compatible to the diagnosis and there were more than 3 abnormal laboratory findings out of the following 5, which were platelet count, PT,... |
Small for gestaional age (SGA) is an entity which we have been slow to recognize in both pediatrics and obstetrics, despite its common occurrence and rather dramatic clinical manifestations. The goal of this study is to be enable all physicians involved in perinatal medical care focus their attention on the fact that infants of the same size but very different gestational ages are... |
To evaluate the correlation between clinical and ultrasonographic findings, 79 consecutive brain ultrasonographic examinations were performed in the 50 prematurity and 29 SGA. Statistical significance was not detected about sex ratio, hemoglobin and hematocrit, Apgar score and maternal age between the prematurity and SGA. Incidence of ICH was 66% in the prematurity and 48% in the SGA. According to Papile’s grading system, Grade 1 was... |
Clinical, Bacteriologic and radiologic studies were performed in 321 infants and childen with urinary Tract Infection who were diagnosed at Department of pediatrics, Haesung Hospital from Jan. 1984 to Dec. 1988. The results were summarized as follows: 1) The incidence of urinary tract infection was highest in children below the age of one year, the rate then decreased with age. Among the total 321 cases,... |
Although the exact mechanism of the immunologic injury is unknown, the pathogenesis of the Guillain-Barr受 syndrome is explained as an autoimmune attack directed against to peripheral nervous myelin. So plasmapheresis is tried for treatment of Guillain-Barr즌 syndrome. Authors analysed 12 cases af Guillain-Barr受 syndrome who were treated with plasmapheresis and compared the results with that of the 13 cases, treated with conventional therapy. Duration between... |
Children with Down syndrome have an increased incidence of acute leukemia. Infants with Down syndrome are also at risk of developing a transient myeloproliferative disorder indistinguishable from acute nonlymphocytic leukemia (ANLL) except by its eventual clinical recovery. We observed 11 patients with acute leukemia or transient myeloproliferative disorder in Down syndrome who had admitted to the Departmetn of Pediatrics, Seoul National University Children’s Hospital,... |
A clinical study was done on 96 cases of goiter in children which were diagnosed at pediatric department of Kwangju Christian Hospital during the period form January 1985 to December 1988. The observed clinical data were summarized as follows: 1) Preponderately femalels were affected with the sex ratio of 1:6.7. The majority of cases (78.2%) were around puberty. 2) On physical examination, 59 cases (85.5%) were found... |
The congenital lactic acidosis represent a sizable group of metabolic disorders. They are in all likelihood genetically determined, and they are clearly heterogenous. They may be considered broadly as disorders of pyruvate metabolism in which there are two general categories: defects in gluconeogenesis and defects in pyruvate oxidation. We experienced a case of congenital lactic acidosis in neonate who was diagnosed by urinary organic acid... |
Acrdermititis enteropathica is a rare autosomal recessive disorder of zinc absorption and its cardinal symptoms appear at the time of weaning from breast milk which has been referred to as most appropriate formula to prevent and treat this disease. However, recent reports presented Transient Symptomatic Zinc deficiency (TSZD) in infants fed breast milk whom they treated with transitory zinc supplement with no recurrence. We experienced... |
Interstitial pulmonary fibrosis is a rare, diffuse lug disease which has a tendency to destroy the lung architectures by consequent healing with progressively severe fibrosis. We report with a brief review of literature, one case of a 7-year old female with the typical pictures of interstitial pulmonary fibrosis, histologically on open lung biopsy, and clinically presenting with chronic respiratory difficulty but without definite symptoms... |
This is a report of 10 years old boy whose complete total ophthalmoplegia, ataxia and areflexia (Fisher syndrome) were the outstanding clinical features. |
We experienced two cases of Werdnig-Hoffmann Disease in a 23 minths old boy & 15 months old boy with the complaint of progressive muscular weakness on both extremities. There development has been almost normal until 3 month of life in case 1 and until 8 month of life in case 2. Diagnosis was based on clinical features, electromyography and muscle biopsy. We report... |
We experienced a case of Beck with-Wiedemann Syndrome. This 1-day-old female neonate manifested gigantism, macroglossia, anomaly of the umbilical cord, hemihypertrophy, mild he- patomegaly, congenital heart disease and severe hypoglycemia. A brief review of related literature was made. |
The hybrid acute leukemia is defined as acute leukemia with both myeloid and lymphoid features. We experienced and report two cases of hybrid leukemia which were identified by morpholgy, cytochemical stain, reactivity with monoclonal antibody, analysis of immunoglobulin and T cell receptor genes rearrangement in 14 years old boy and 10 years old girl. |
Adrenocortical carcinoma is a rare disease in childhood. Most of these carcinomas are functional, produc- ing endocrine abnormalities such as Cushing syndrome, virilization, precocious puberty, hyperaldosteronism or feminization. We experienced a case of adrenocortical carcinoma in a 12 month old male infant who exhibited features of Cushing syndrome, Virilization, precocious puberty and hyperaldosteronism, which were due to functional adrenocortical carcinoma. Microscopic examination revealed cellular pleomorphism... |
The authors experienced a case of insulin-dependent diabetes mellitus with hypothyroidism. We recommend that all patients with insulin-dependent diabetes mellitus be screened for thyroid mi- crosomal antibody and that those patients found to have thyroid microsomal antibody be followed annually for determination of free T4 and TSH values. We report this case with a review of related literatures. |