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Pulmonary valve stenosis was relieved by balloon dilatation during cardiac catheterization on 58 children aged 8 months to 15 years, mean 6.2 years. Pulmonary valve diameter was estimated by two-dimensional echocardiogrphy to assist in the choice of balloon size. Before dilatation the transpulmonary systolic pressure gradients ranged from 15 mmHg to 250 mmHg. There were significant reduction in the transpulmonary systolic pressure gradients immediately after... |
The two dimensional echocardiographic technique for detecting coronary artery aneurysms was performed in 62 cases with mucocutaneous lymphnode syndrome. Of 62 patients with MCLS, coronary artery aneurysms were detected as large echo-free space in 8 patients. It was found that coronary artery aneurysms usually developed during the acute stage of the illness, and regressed gradually thereafter. Most aneurysms disappeared in 6 months. Therefore, Echocardiography is... |
Chilhood bronchial asthma tends to be increased annually and overall incidence is about 3-10% of childhood age. Asthma is a troublesome disease during school life and nocturnal attacks often frighten the family. Asthma is a chronic obstructive pulmonary disease but usually self remmission with or without specific treatment. Asthma can be triggered by a variety of causative facotrs such as extrinsic, emotional, environmental,... |
We have compared recurrent wheezing group with non-recurrent wheezing group of 91 cases on the aspects of clinical and laboratory findings, were admitted to the Department of Pediatrics, Won Kwang University Hospital with the impression of acute bronchiolitis from Jan. 1983 to Feb. 1986 The results were as follows; 1) The incidence of recurrent wheezing was 28.6%. 2) Sex incidence of recurrent wheezing was high in male.... |
Auditory Brainstem Response(ABR) has been found to be useful for evaluating objective assessment of hearing thresholds, maturation of the brainstem and neurological disorders in the brainstem. Therefore it is essential to define normal ranges and accurate changes in the wave form of the ABR in children. This study was undertaken with the analysis of 243 ABR in children with normal otological, developmental, neurological... |
We reviewed 24 patients with congenital hypothyroidism to observe the etiology, clinical symptoms and signs, bone age, height age, the degree of mental retardation and growth velocity after treatment form Jan. 1983 to June 1987. The results were as follows: 1) The male to female ratio was about 1:3.8. The cases diagnosed under 1 year old were only 12.5%. 2) In etiologic classification, thyroid dysgenesis... |
We experienced an outbreak of Serratia marcescens septicemia during a 2-month-10-day period (Apirl the 10th, 1985-June the 6th, 1985) in the Chonju Presbyterian medical center, pediatric ward. The clinical and bacteriological features of 22 patients with septicemia were described. There were 25 bacterial isolates from 22 patients. Twenty cases of 22 patients recovered, while 2 patients died, both premature infants. This indicated the seriousness... |
The incidence of end stage renal disease (ESRD) in childhood seems to be around two to three children per million population per year and the most frequent diagnoses of ESRD in pre-teen patients are congenital and dysplastic diseases. Renal transplantation may be the preferred method for the treatment of ESRD especially in children not only becauses of better development and linear growth, but also... |
Malignant mesenchymoma of the liver is extremely rare in childhood. It is formed by 2 or more unrelated mesenchymal tissues, chacterized by rapid growth and poor responsiveness to all modes of therapy. We experienced a case of malignant mesenchymoma of the liver in a 11-year-old boy who was admitted because of abdominal pain, anorexia, nausea and vomiting. Radiographic examinations showed a space occupying lesion... |
A case of the Naumoff type (type 3) of short rib-polydactyly syndrome is reported. The skeletal changes included bulging forehead, flat occiput, short cranial base, extremely short horizontal ribs, abnormal vertebrae, and post-axial polydactyly. Microscopically, cartilage showed markedly stunted and disorganized endochondrial ossification. Extraskeletal manifestation were cleft palate, pulmonary hypoplasia, hydropelvis and hydroureter with narrowing of ureterovesical junction. Differentiation from other type of short rib-polydactyly syndrome... |
We have experienced a case of tubular duplication of the ileum in a 5 year old female patient. She had an egg sized abodminal mass for 4 years and postprandial abdominal distension for 2 years in R. L.Q. of abdominal cavity. Operation revealed tubular duplicated blind intestine, measuring 21 cm in length. The pathologic diagnosis confirmed duplication of the ileum. Treatment were resection of... |
Isoimmune thrombocytopenic purpura is an uncommon cause of purpura in the newborn infant, caused by fetal-maternal platelet incompatibility. The maternal isoantibodies against fetal platelet antigens, which are lacked in mother’s platelets, cross placenta and cause destructions of baby’s platelet. A bady bom with IITP was diagnosed in the first day of life and treated successfully with platelet concentrate of mother’s blood. |
Congenital hepatic fibrosis is a relatively rare disease of liver in children and young adults, manifesting a heredofamilial tendency, that is characterized by hepatosplenomegaly, protal hypertension and frequent renal involvement. A generalized portal and interlobular fibrosis of liver are characteristic finding on microscopy, with relative preservation of hepatocyte and liver function. Recently, we have experienced a case of congenital hepatic fibrosis in a... |
We experienced a case of type A Niemann Pick disease in 13 month female baby. She showed marked hepatosplenomegaly, developmental regression and apathy. Fundoscopic examination revealed a cherry red spot in the macula. Numerous foamy histiocyte were seen in bone marrow. Autopsy finding revealed that liver, spleen, thymus, lymph node, lung and brain were involved. Liver showed fatty change. Generalized muscular atrophy and patch... |
A 4 day old male patient was admitted to our hospital due to jaundice, poor feeding and abdominal distention. His clinical features and peripheral blood smear revealed congenital myeloblastic leuke- mia which confirmed by autopsy. Chromosome study showed 47, XY, +21 in Karyotype. We report this case with review of literatures. |
Two cases of Wilson’s disease were experienced, which showed symptoms of hepatic dysfunction, Kayser-Fleischer ring and decreased serum ceruloplasmin and increased urine copper excretion. Case 1: An 9 years old boy was admitted with abdominal distension and general edema, he had low serum ceruloplasmin levels (7.0 mg%) and high levels of urinary copper (2020 必g/24 hrs) and increased transaminase levels (292 U/L of SGOT,... |