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Case Report
A Case of Ornithine Transcarbamylase(OTC) Deficiency
Soonhak Kwon, Yejhin Lee, Byung-Ho Choe, Sangkwon Lee
Clin Exp Pediatr. 2000;43(1):123-127.   Published online January 15, 2000
OTC deficiency is an X-linked disorder in which the synthesis of urea is impaired. OTC catalyzes the synthesis of citrulline from carbamyl phosphate and ornithine. Complete or partial deficiencies of this enzyme may lead to Reye syndrome like picture such as encephalopathy, hepatic dysfunction, hyperammonemia, etc. We recently had a case that was presented as recurrent Reye syndrome, and was...
Original Article
Clinical Observation on Reye syndrome According to the Onset of Age in Children
Kyung Hee Kim, Baik Hee Lee, Myung Ik Lee, Don Hee Ahn, Keun Chan Sohn
Clin Exp Pediatr. 1992;35(6):788-794.   Published online June 15, 1992
A clinical observation according to the age of onset was made on 40 children with Reye syndrome who had been admitted to pediatric department of National Medical Center during 11 year period from January 1979 to December 1989. 1) Annual distribution showed the largest number in 1982. There was no significant difference in seasonal distribution. 2) Cases of infant comprised 22 (55.0%)...
Factors Influencing the Prognosis of Reye Syndrome.
Chang Ho Hong, Heung Dong Kim, Pyung Kil Kim
Clin Exp Pediatr. 1987;30(11):1252-1258.   Published online November 30, 1987
While the etiology of Reye syndrome is still unknown, wide variations in both the clinical spectrum and the therapeutic outcome of patients have been noted. We reviewed the cases of 42 Reye syndrome patients who were admitted to Young Dong Severance Hospital during the period from April, 1983 to July, 1986 and analyzed factors influencing the prognosis of Reye syndrome. The patients were divided...
A Clinical Studey on Reye Syndrome.
Myung Ho Oh, Hung Sub Choi, Chang Hwi Kim, Sang Jhoo Lee
Clin Exp Pediatr. 1987;30(11):1243-1251.   Published online November 30, 1987
We took clinical study for 47 cases of Reye syndrome at S.C.H. University Hospital during last 8 years from Jan:, 1979 to Dec., 1986. The results obtained were as follows; 1) There was no significant difference in annual incidence and the seasonal incidence was highest in sumer and autumn. 2) The sex ratio of male to female was...
A Clinical Study on Reye Syndrome.
N C Kim, C H Kim
Clin Exp Pediatr. 1983;26(2):158-164.   Published online February 28, 1983
We analyzed 15 infants and children who were admitted and diagnosed as Reye syndrome. at Gu Mi Soon Chun Hyang Hospital during the period of 9 months from Feb. 1981 to Oct. 1981 The results were as follows. 1) The cases of Reye syndrome were 15 patients (1. 6%) among 579 hospitaHzed patients and 4 patients (26.7%) died of Reye syndrome. 2) It affected male...
Case Report
Two Cases of Postvaricella Reye Syndrome.
Won A Park, Sang Keun Chi, In Ho Kim, Churl Young Chung
Clin Exp Pediatr. 1982;25(5):528-532.   Published online May 31, 1982
Authors observed two cases of Reye syndrome in 7 and 8 year old male patients who had begun to vomit after chickenpox. The interval between the onset of varicella rash and encephalopathy of Reye syndrome was 4 days in both these cases. The initial laboratory findings revealed increased serum transaminase and blood ammonia levels which returned to normal on 18...