Purpose : We will present our mid-term result of transcatheter closure of PDA with Duct-Occlud device(pfm. AG. Germany) after 12 months follow up and report the problems during the procedure. Methods : In total 154 patients, the Duct-Occlud devices were inserted in our institute from March, 1996 to August, 2002. Three types of Duct-Occlud device, i.e standard, reinforced, reinforced reverse cone... |
Purpose : This study was performed to follow the natural course and size change of isolated atrial septal defect(ASD) secundum. Methods : Among the newly diagnosed with ASD secundum at the division of pediatric cardiology in Yonsei cardiovascular hospital from January 1996 to December 2000, 89 patients with pure ASD secundum were checked by the serial echocardiographic evaluation to measure... |
Purpose : We have performed an analysis on patients who received Rastelli operation in our institute and reviewed their progress postoperatively. Various factors with suspected relationship to the outcome have been considered to help in future treatment and follow-up. Methods : We analyzed retrospectively 43 patients who either received Rastelli operation in Yonsei University Cardiovascular Center from March 1995 to April... |
Purpose : The actual clinical examples of co-appliance of catheter intervention with surgical procedures in the treatment of pulmonary atresia with an intact ventricular septum(PA/IVS) which we have experienced in our institution are here shown, and the anatomical and hemodynamical profiles between each method is compared. Methods : Medical records of 33 patients with PA/IVS who underwent various treatment from January,... |
Purpose : Intravascular stent implantation for the treatment of postoperative branch pulmonary artery(PA) stenosis has been used successfully. However, the cross sectional area of contralateral branch PA does not regress in spite of the successful dilation of the stenotic branch PA after stent implantation. We analyzed the morphologic and hemodynamic factors on the size of branch PA after successful... |
Purpose : Since the successful application of total atrio-pulmonary connection(TAPC) to patients with various types of physiologic single ventricles in 1971, post-operative survival rates have reached more than 90%. However some patients have been shown to present with late complications such as right atrial thrombosis, atrial fibrillation and protein losing enteropathy eventually leading to re-operation to control the long-term complications.... |
Purpose : This study was undertaken to analyze and compare the effects of percutaneous balloon angioplasty(BAP) on postoperative re-coarctation and native coarctation of the aorta(CoA) and to thereby contribute to the development of treatment methods for CoA. Methods : The subjects in this study were 21 children who had undergone BAP from Jan. 1996 to Dec. 2000 in the Division of Yonsei Pediatric Cardiology.... |
Purpose : Pulmonary artery stenosis is mainly complicated by aortopulmonary shunt or total correction of tetralogy of Fallot(TOF). Results of surgical angioplasty are poor and the success rate of balloon angioplasty is 53-72%. Endovascular stents have been applied to these lesions. The purpose of this study is to evaluate the early results of stent implantation in postoperative pulmonary artery stenosis... |
Purpose : Low-birth-weight(LBW) neonates often need multiple transfusions during their neonatal period. The routine use of the 500ml mono-bag system in Korea, even in neonatal transfusions, results in a great waste of blood and exposes the neonate to multiple blood donors. To reduce the waste of blood and the number of exposures, we used quadruple blood bags in the transfusion... |
Kawasaki disease is an acute illness of early childhood, especially less than 5 years of age, characterized by prolonged fever(> 5 days), changes of lips and oral cavity, changes of peripheral extremities, polymorphous skin rash, bilateral conjunctival congestion and acute nonpurulent cervical lymphadenopathy. Usually, the recurrence of Kawasaki disease is not frequent. It is thought that the factors in recurrence of Kawasaki disease was... |
Unilateral absence of pulmonary artery(UAPA) is a rare disease. We experienced 2 cases of UAPA in 5 month-old male patient and 16 year-old female patient with the chief complaint of dyspnea. Lung perfusion scan, cardiac catheterization with pulmonary and aortic angiography confirmed the diagnosis of UAPA. |
Purpose : Subpulmonic ventricular septal defect is clinically important because the risks of aortic regurgitation and endocarditis are substantially increased. This study was conducted to evaluate the effect of hemodynamic changes induced by structural anomalies of aortic valve on the surgical outcome. Methods : This clinical study was done by reviewing the medical records of 124 patients who were diagnosed and surgically managed at the... |
Purpose : Recently, non-operative transcatheter management of congenital heart defects h as increased due to their effectiveness and safety being acknowledged. In the case of secundu- m atrial septal defect(ASD), closing devices have been developed since 1974 and have been u sed clinically. The authors, having tried the "Buttoned" device which was developed in 1990 an d having succeeded in... |
Aneurysms of the coronary arteries are rare. They may be due to atherosclerosis, mucocutaneous lymph node syndrome, mycotic emboli, syphilis or trauma and occasionally they are congenital. The prognosis appears to be poor and death can occur suddenly from rupture of the aneurysm, peripheral coronary embolism or bacterial endocarditis. Recently surgical treatment has been successful In a 5 year old patient with... |
The persistend left superior vena cava(LSVC) is not rare cardiovascular developmental anomaly occurring both in association with congenital heart disdease and as an isolated anomaly of no hemodynamic importance. We have studied 73 cases of the LSCV out of 1,060 cases of congenital heart disease catheterized at Yonsei Cardiovascular Center. We conducted the study with a view point of position of... |
The hemodynamic feature of the tetralogy of Fallot (TOF) is best characterized by equality of left and right ventricular peak systolic pressure. The interventricular septum is flattened and thickened. Even after the right ventricular pressure is normalized in the postoperative period, the morphological abnormality continues for some time. We have analyzed the morphological changes of the IVS echocardiographically after total... |
The congenital diverticulum of ventricle is a rare cardiac malformation arising from the left or right ventricle, the former being more common. Ventricular diverticulum is usually associated with other anomalies including intracardiac, midline thoracic, diaphragmatic and abdominal wall defect. The authors experienced a case of congenital diverticulum of left ventricle in nine month-old female infant. Left Blolock-Taussig shunt operation was done... |
Double outlet right ventricle, a complex of congenital cardiac anomalies in which both great arteries arise wholly or in large part from the morphologic right ventricle presents diverse clinical manifestations according to the morphological characteristics. Eighty cases with DORV were diagnosed and operated at Yonsei Cardiovascular Center from 1988 to 1992. The analysis of the morphological characteristics of this anomaly and... |
Morphological evaluations accounting the associated anomalies were performed in the 60 cases of tricuspid atresia, diagnosed at Divsion of Pediatric Cardiology. The following results were obtained. 1) Twenty one out of the 6 cases had transposition of the great vessels, among which 8 cases were in complete A-transposition. 2) Seven cases were associated with pulmonany atresia, in 1 case, aorts arise from... |
Infrahepatic interruption of the inferior vena cava with azygos continuation is elatively infrequent cardiovascular developmental anomaly occurring both in association with congenital heart disease and as an isolated anomaly of no hemodynamic importance. During the past 5years, we observed 38cases of infrahepatic interruption of IVC with azygos continuation out of 2,397 cases of congenital heart disease catheterized at Yonsei... |
Many forms of congenital heart disease are arrests in normal development. An understanding of the relevent embryology and pathology is basic to the understanding, accurate diagnosis, and successful management of congenital heart disease. The heart appears on the 18th day of life and its formation is normally completed by about the 40th day of life when the embryo is approximately... |
Exercise tolerance tests were performed using treadmill in 21 patients with tetralogy of Fallot (TOF) repaired earlier (4.8 years in mean) and 10 subjects with small ventricular septal defect or normal heart, aged 8-16 years. Pre and postexercise echocardiography and cardiac catheterization were also performed and the hemodynamic data were compared with exercise parameters. The following results were obtained. 1)... |
This is a 28-year analysis of 5,653 cases with congenital heart disease who underwent cardiac catheterization at Yonsei Medical Center from 1964 to 1991. Form 1964, there was a steady increment in the number of catheterized cases with CHD until the late 1970's when the patients population began to increase rapidlly. This was undoubtedly set off by the introduction of the... |
Heart failure is the state in which heart cannot produce the cardiac output required to sustain the metabolic needs of the body without evoking certain compensatory mechanisms. As these mecha- nisms become ineffective, increasingly severe clinical manifestations result. The diagnosis of conges- tive heart failure relies on several sources of clinical findings, including history, physical examination, and chest X-rays. For lack of uniform diagnostic... |
A clinical study was made on 98 cases of measles patients admitted to YoungDong Severance Hospital during the period of 7 months from June to December 1989. The patients with measles were evaluated for presence of measles specific IgM antibody in serum, clinical symptom and vaccination history. We obtained the following results: 1) Out of 98 patients, 62 patients (63.3%) were vaccinated children and 36 patients... |
We experienced a case of adult type Gaucher’s disease in a 2 year 9 month old female. The patient had hepatosplenomegaly with anemia and characteristic Gaucher cells in bone marrow aspiration and biopsy of liver and spleen. Diagnosis was confirmed by demonstration of β-glucosidase enzyme deficiency in circulating leukocytes. Partial splenectomy was followed by improvement of anemia and thrombocytopenia. A brief review of literature was done. |
The False tendon is an anomalous chordae tendinae which attaches to abnormal sites in left ventricle. We studied the incidence of false tendon and relationship of the false tendon, functional murmur and arrhythmias using echocardiography. The results were as follow; 1) We found false tendons in 42 cases of total 307 cases, 13.6% 2) In group I (the patients who have congenital heart disease), the incidence of... |
Mitral atresia is a rare and fatal congenital heart disease. We experienced a case of mitral atresia associated with double outlet right ventricle(S.D.S). atrial septal defect and multiple ventricular septal defect in a 50 day old female infant. which was diagnosed by echocardiogram and confirmed at autopsy. |
We experienced a case of truncus arteriousus associated with interrupted aortic arch, ventricular septal defect and patent ductus arteriosus. A 5 month old boy had complained of rapid respiration and feeding difficulty since birth. There was no visible cyanosis or clubbing toes and nails. There was a grade 2 〜3 ejection systolic murmur with maximum intensity at the left lower sternal border. Diagnosis was... |
Kawasaki disease, first reported in Korea in 1973, is now one of the disease commonly encountered in pediatric age group. It presents systemic symptoms including abdominal ones such as pain, nausea and vomiting, etc. There have been several case reports of hydrops of the gallbladder occuring concurrently with Kawasaki disease, and the abdominal symptoms of the disease are known to correlate with hydrops of... |