Purpose : Despite recent advances in pulmonary hypertension management and surgery, appropriate guidelines remain to be developed for operability in congenital heart disease with pulmonary artery hypertension (PAH). Our aim was to evaluate clinical outcomes of patients with severe PAH who underwent surgical closure of left-to-right shunt lesions (LRSL) on the basis of pulmonary reactivity. Methods : We retrospectively reviewed 21... |
Purpose : This study investigated the clinical course and prognostic factor of very low birth weight infants (VLBWI) with hemodynamically significant congenital heart defects (CHDs). Methods : Medical records of 1,098 VLBWI with birth weight <1,500 g who had been admitted to the neonatal intensive care unit of Samsung Medical Center from October 1994 to December 2007 were reviewed retrospectively. The... |
Purpose : The aim of this study was to investigate the epidemiologic status of Kawasaki disease (KD) in infants ≤6 months of age. Methods : For the epidemiologic study of KD in Korea, data from 22,674 KD patients were collected from 1997 to 2005 on a 3-year basis by a retrospective survey. From this survey, data of 1,739 KD patients ≤6... |
Purpose : The purpose of this study was to investigate the relationship between depression and resilience in adolescents with congenital heart disease(CHD) and to identify the variables associated with depression. Methods : The Resilience Scale(cronbach’s α=0.92), Children's Depression Inventory(cronbach’s α= 0.72) and Maternal Behavior Research Instrument(cronbach’s α=0.88) were applied and analyzed to assess depression and resilience among 231 adolescents after... |
Purpose : The aim of this study was to investigate the epidemiologic and clinical profiles of Kawasaki disease(KD) in children 8 years of age and older. Methods : For the epidemiologic study of KD in Korea, data of total 15,692 KD patients were collected from 1994 to 2002 on a 3 year basis, by the retrospective survey. Among them, data of... |
Purpose : This study was performed to find the chief clinical problems associated with the ages of adult patients of tetralogy of Fallot(TOF) who had undergone total correction. Methods : Of the 30 patients who were registered at the Grown-Up Congenital Heart Disease (GUCH) Clinic of Samsung Medical Center for TOF, a retrospective investigation was carried out on 28 patients who... |
Purpose : The outcomes of infants weighing less than 1,500 gm(very low birth weight infant : VLBWI) reflect recent progress in neonatal intensive care. In this study, we analyzed changes over time in survival rate and morbidity of VLBWIs during the past seven years. Methods : A retrospective review of medical records was analyzed for VLBWIs admitted to the neonatal intensive... |
Purpose : In children, dysphagia is a common cause of recurrent pneumonia and malnutrition and can be fatal. However, till now no studies were performed concerning the clinical investigation of dysphagia in Korea. Methods : In this study we evaluated the clinical manifestations of dysphagia in children with an age range between 1 month and 12 years by reviewing the... |
Purpose : The aim of this study was to assess the involvement of several organs patients with Marfan syndrome in Korea. Also the clinical features in childhood patients with Marfan syndrome were assessed. Methods : Thirty-eight cases of Marfan syndrome were enrolled in this study. Clinical evaluations of the musculoskeletal, cardiovascular and occular system were performed in all cases. Results : The... |
Purpose : It has been stressed that age itself as well as multiple organ failure are important prognostic factors in acute renal failure(ARF) in children. This study was performed to find out the significance of age factor and underlying disease of ARF in children. Methods : We tried to review 58 pediatric ARF cases, retrospectively, in the pediatric intensive care unit(excluding... |
Purpose : We have assessed the clinical usefulness of solid maker transit technique and Barr-score in 31 patients with idiopathic constipation (male:female; 17:14, mean age; 6.7 years, range 1.4-12 years). Methods : All patients underwent full history taking and physical examination including rectal examination. On first visit to gastroenterology clinic a plain abdominal film was taken for Barr-score which evaluated by two observers without the... |
Nitric oxide, an endothelium-derived relaxing factor, is a selective pulmonary vasodilator. We have built and settled down the delivery system of nitirc oxide gas inhalation for the first time in Korea. Two newborn babies delvelped near fatal pulmonary hypertension after surgical repair of a congenital diaphragmatic hernia. All conventional therapeutic measures failed. So we decided to attempt to use of nitric oxide gas for... |
Purpose : In the Spring 1995, there was an outbreak of adenoviral infection, which caused four death out of ten patients with adenoviral pneumonia in our hospital. Clinical courses of ten patients with severe pneumonia were similar each other, and two were confirmed as adenoviral pneumonia by postmortem autopsy. Although not proven, we believe eight patients had adenoviral pneumonia. Therefore, we report clinical features... |
Atrial flutter is an infrequent, but potentially unstable tachyarrythmia that occurs in pediatric ages. Transesophageal atrial pacing was used for treatment of 10 episodes of atrial flutter in 7 patients. At the time of atrial flutter conversion, patients were 6 days to 14 years old. 6 patients had associated with congenital heart disease. The atrial cycle length of atrial flutter ranged from... |
Children with cyanotic congenital heart disease (CCHD) and secondary polycythemia exhibit increased susceptibility to hemorrhage or thrombosis. The hemostatic disorder manifests itself by the occurrence of excessive hemorrhage after surgery, and by increased incidence of cerebrovascular accident of a thrombotic nature during life. To assess whether the severity of polycythemia in children with CCHD is correlated with coagula- tion abnormalities, hematologic studies with preoperative and... |
The scimitar syndrome, a rare complex anomaly, consists essentially of an anomalous pulmonary vein draining whole or part of right lung into inferior vena cava and its curved Turkish sword (scimitar) like appearance has provided the name of this syndrome. Associated anomalies are frequent, such as hypoplasia of the right lung and right pulmonary artery, abnormalities of bronchial architecture and lobation, rightward displacement of... |
To assess the VSD type of TOF and relationship between VSD type of TOF and pulmonary valve stenosis, small pulmonary valve annulus, and pulmonary artery anomaly, we analyzed 256 cases of surgically confirmed TOF patients. The summary of observation is as follows; 1) Four tytes of VSDs were found. The most frequent is perimembranous (PM) VSD of which incidence is 75.7% (159/210), second most... |
During the period of 2 years, between January 1986 and December 1987, 36 patients, aged 2 years to 18 years, with congenital pulmonary valve stenosis(PVS) (with peak systolic transvalvar gradient over 30 mmHg) underwent percutaneous transluminal balloon valvuloplasty(TBV) at Sejong General Hospital m Korea. Of a group of 36 patients, 26 were treated successfully by the conventional balloon valve dilatation technique, and 6 were treated... |
Acute Leukemia is the most common among malignant disease in childhood, and the loss of normal hematopoiesis by proliferation of leukemic cells and the chemotherapy result in immunosuppression and the reduction of red blood cells, normal white blood cells and platelets. The children with acute leukemia may succumb to the disease due to infections, hemorrhage, other complications, or the progression... |
The authors experienced a case of cerebral paragonimiasis with severe eosinophilia in a 13 year old female patient. Since several years ago, she frequently drank spring water with her family, especially, with her father. She came to the hospital because of speech disturbance, weakness of right upper extremity and maculopapular skin rashes of lower half of body. In her family history,... |
During the period of 4 years from October, 1980 to September, 1984, 28 cases with septal aneurysm in membranous ventricular septal defect were observed and evaluated at Hanyaeng University Hospital, and those were confirmed by LV angiogram and/or 2D-echocardiogram. We also correlated the findings of aneurysm of the membranous septum with clinical, electrocardiographic and hemodynamic data for use in noninvasive... |
During a period of IOV12 years, from April, 1974 to July, 1984, 92 cases under 15 years of age with isolated patent ductus arteriosus were observed and evaluated pre- and postoperatively at pediatric department, Hanyang University Hospital, and those were confirmed by cardiac catheterization and/or surgery. The summary of observation made is as follows: 1)The sex ratio of male to female... |
Authors experienced three cases of arrhythmia which were assumed to be present from their fetal lives. One of cases was congenital complete heart block with Adams-Stokes attacks who had the history of severe fetal bradycardia. The other two cases had benign supraventricular ectopic beats with spontaneous recovery within two months of age. Fetal tachycardia was observed in one case with multifocal... |
During the period from May 1981 to Feb. 1984, authors experienced 15 cases of double chambered right ventricle (D.C.R.V.) at Hanyang University Hospital. Among these 15 cases of D.C.R.V., 13 cases were confirmed by open heart surgery. We analysed the physical characteristics and echocardiographic, cardiac catheterization, angiographic and operative findings. Results are as follows; 1) Authors observations suggest that right ventricular obstructing... |
To assess the validity of Echocardiographic criteria for pulmonary arterial hypertension we studied pulmonary valve motion in 75 congenital heart disease children. 75 patients were divided into two groups, A and B. The group A consisted of 39 patients who had normal pulmonary arterial pressure, group B consisted of 36 patients who had pulmonary arterial hypertension(pulmmonary artery mean pressure more... |
This report was conducted to estimate the relative incidence of acute viral hepatitis (all were under 15 years of age. Who were admitted to the Pediatric Department, Hanyang University Hospital during the period from March 1982 to August 1983 were evaluated. The following results were obtained. 1)The sex ratio of of male to female was 1.34 : 1. 2)The incidence... |
The authors experienced a case of familial Treacher-Collins syndrome in 24 years old mother and 2 months old male baby confirmed by typical facial appearance such as antimongoloid slant, coloboma, macrostomia and micrognathia and X-ray findings. We reviewed the literatures briefly. |
We had experienced a case of meningomyelocele combined with Arnold-Chiari malformation. This neonate had her birth weight of 2,960 gm after 41 weeks of gestation. At birth, he noticed the Apgar Score of 0, so he was resuscitated immediately. On physical examination, he noticed large head and fist sized mass on back. Inspite of intensive care, he was expired at 2... |
The authors experienced a case of acute renal failure following nephrectomy of soliary kidney in a 9 month old girl. Her chief complaints on admission were total anuria for 10 days and gastrointestinal bleeding for 7 days. On physical examination, she were noticed drowsy mental state, generalized edema and pale appearance. Laboratory date and management;Hb 3.4mg%,BUN 150mg%,she was performed peritoneal?dialysis... |