Many forms of congenital heart disease are arrests in normal development. An understanding of the relevent embryology and pathology is basic to the understanding, accurate diagnosis, and successful management of congenital heart disease. The heart appears on the 18th day of life and its formation is normally completed by about the 40th day of life when the embryo is approximately... |
Exercise tolerance tests were performed using treadmill in 21 patients with tetralogy of Fallot (TOF) repaired earlier (4.8 years in mean) and 10 subjects with small ventricular septal defect or normal heart, aged 8-16 years. Pre and postexercise echocardiography and cardiac catheterization were also performed and the hemodynamic data were compared with exercise parameters. The following results were obtained. 1)... |
This is a 28-year analysis of 5,653 cases with congenital heart disease who underwent cardiac catheterization at Yonsei Medical Center from 1964 to 1991. Form 1964, there was a steady increment in the number of catheterized cases with CHD until the late 1970's when the patients population began to increase rapidlly. This was undoubtedly set off by the introduction of the... |
Heart failure is the state in which heart cannot produce the cardiac output required to sustain the metabolic needs of the body without evoking certain compensatory mechanisms. As these mecha- nisms become ineffective, increasingly severe clinical manifestations result. The diagnosis of conges- tive heart failure relies on several sources of clinical findings, including history, physical examination, and chest X-rays. For lack of uniform diagnostic... |
The False tendon is an anomalous chordae tendinae which attaches to abnormal sites in left ventricle. We studied the incidence of false tendon and relationship of the false tendon, functional murmur and arrhythmias using echocardiography. The results were as follow; 1) We found false tendons in 42 cases of total 307 cases, 13.6% 2) In group I (the patients who have congenital heart disease), the incidence of... |
Mitral atresia is a rare and fatal congenital heart disease. We experienced a case of mitral atresia associated with double outlet right ventricle(S.D.S). atrial septal defect and multiple ventricular septal defect in a 50 day old female infant. which was diagnosed by echocardiogram and confirmed at autopsy. |
We experienced a case of truncus arteriousus associated with interrupted aortic arch, ventricular septal defect and patent ductus arteriosus. A 5 month old boy had complained of rapid respiration and feeding difficulty since birth. There was no visible cyanosis or clubbing toes and nails. There was a grade 2 〜3 ejection systolic murmur with maximum intensity at the left lower sternal border. Diagnosis was... |
A clinical assessment of the 30 patients with dilated cardiomyopathy who were admitted to the Department of Pediatrics, Yousei University Hospital from January, 1980 to June, 1986 was perfor- med. The results were as follows: 1) Among 30 patients of dilated cardiomyopathy, 11 cases (36%) were younger than 1 year of age and 6 cases (20%) were 1-2 years of age on admission. The male to... |
The two dimensional echocardiographic technique for detecting coronary artery aneurysms was performed in 62 cases with mucocutaneous lymphnode syndrome. Of 62 patients with MCLS, coronary artery aneurysms were detected as large echo-free space in 8 patients. It was found that coronary artery aneurysms usually developed during the acute stage of the illness, and regressed gradually thereafter. Most aneurysms disappeared in 6 months. Therefore, Echocardiography is... |
In selected cases, early corrective surgery is indicated in the management of infants with moderate or large ventricular septal defects. The risks of any surgical procedure in infancy are acknowledged to be great and should be avoided if possible. However, these surgical risks are justified when the patients have intractable congestive heart failure, marked growth retardation, recurrent prolonged lower respiratory... |
We experienced a case of coarctation of the aorta with aneurysmal dilatation which was located in aortic arch, who was a 13 year old male.On physical examination on admission, pulses were weak in right radial artery and in both femoral artery. Blood pressure measured 100/70 mmHg in right arm, 100/70 mmHg in left arm, 130/110 mmHg in right leg and 130/110... |
Unilateral Absence of Pulmonary Artery(UAPA) is a rare disease. It is characterized by no specfiic cardiopulmonary symptoms in general. We experienced a case of UAPA in a 9 year-old female patient with the chief complaint of abnormal chest Xray finding. Lung perfusion scan, cardiac catheterization with pulmonary and aortic angiography confirmed the diagnosis of right side UAPA. |
This study is a report of two cases of vascular ring that were experienced at Yonsei University in 1983 and 1985. The first case was a one-month-old female patient with a double aortic arch and PDA. The main pulmonary artery was connected to the anterior arch by PDA. The anterior arch was larger in diameter than the posterior arch and the descending... |
There are four main groups of clinical manifestations in salmonellosis, gastroenteritis。 enteric fever, localized infection, and chronic carrier state, that may occur individually, simultaneously or consecutively in the course of an infection. The authors experienced a case of salmonella gastroenteritis complicated with empyema of gall bladder in a 12-year-old male patient. The clinical diagnosis was confirmed on the operating table and... |
Coarctation of the aorta is defined as a narrowing of the aorta in the region of its juncture with the ductus arteriosus or its vestige, and is rare in Orient. We have experienced three cases of Coarctation of the Aorta combined with other congenital cardiovascular anomalies and diagnosed by cardiac catheterization and cineangiography. Review of literature was made briefly. |
Clinical problem occuring in the early post operative period after cardiopulmonary bypass may ne related to the altered function of capillary bed which was affected by activation of complement system. This is so called post perfusion syndrome. We selected 20 patients with confirmed congenital heart disease by cariac catheterization. We studied the changes in the C3 , immunolglobulins, total protein,... |
Ivemark’s syndrome is rare disease and characterized by congenital absence of the spleen as sociated with characteristic group of anomalies of the cardiovascular and gastroenteric systems. We had experienced 4 cases of Ivemark’s yndrome: Case 1 had asplenia, situs inversus, dextrocardia, ASD, and pulmonary stenosis; Case 2 had asplenia, bilobulated liver, centraly located stomach but deviated to right side, single... |
Congenital Megacolon is due to congenital defect of the parasympathetic ganglionic cells in Auerbach’s plexus causing constriction anatomically at rectum or rectosigmoid in majority and an abscence of peristalsis and propulsive movement functionally with marked dilatation at the proximal bowel of the defected area. We have experienced 33 caess of congenital megacolon from January, 1957 to December, 1972 and this disease... |
The authers experienced a case of Treacher-Collins syndrome in a 2 day-old Korean newborn. Patient was characterized by antimongoloid slant of the palpebral fissure, lack of development of right auricle, cleft palate and hypoplasia of the facial bone, especially the mandibular and zygomatic bones resulting in micrognathia and “fish-like” facial appearance. The review of literature was made briefly. |
78 cases of neonatal hyperbilirubinemia who had exchange transfusion were studied clinically. They were admitted to Severance Hospital from July 1962 to June 1971 and the results were as follows. 1. They were consisted of 37 cases (47.4%) of ABO incompatibliity, 16 cases of physiologic jaundice (20. 0%), 8 cases of Rh incompatibility (10. 0%) and... |
We had a case of total anomalous pulmonary venous drainage, a 10 years old schoolboy who admitted to our Severance Hospital with chief problems of exertional dyspnea, palpitation, and known congenital heart disease since infancy. We confirmed this case as a total anomalous pulmonary venous connection to persistent left inno minate vein which drains into right atrium, atrial septal defect (secundum... |
Cystic hygroma is a rare disease, but we can easily diagnose it with the naked eye, and it develops mostly within the first 2 years of life. The purpose of this paper is to report 20 cases of cystic hygroma which were treated, as inpatients in the Pediatric or Surgical Departments of Severance Hospital during last 18 years. The conclusions... |
Total 553 cases of acute diarrhea who were admitted to pediatric department of Severance Hospital from Jan. 1967 to Dec. 1971, were subjected in this study. Among these, 116 dysenteric cases (21%) were analysed as followings: 1)The incidence of dysentery was highest from 6 months after birth to 2 yrs., and relatively rare below the 6 months of age. 2) The character... |
Craniofacial dysostosis (Crouzon’s disease) is a rare disease and there is no report of craniofacial dystosis in children in Korea. We experienced a case of Crouzon’s disease in 4 day old male infant with chief complaints of respiratory distress and bilateral exophthalmos since birth. Physical examination showed craniosynostosis, bilateral exophthalmos, external strabismus, bird-like beaked nose, bilateral choanal atresia, high arched palate,... |
Eight of pediatric diabetes insipidus, who have been admitted and treated at Department of Pediatrics in Severance Hospital from Jan. I960 to Dec. 1971, were summarized as follows. 1. Male to female ratio was 3:1. 2. Seven out of 8 cases were between 8 to 10 year of age. 3. Etiologic causes were 2 cases of idiopathic, 2 of craniopharyngioma, 2 of skull fracture and 2 of ... |
Neonatal tetanus is still one of the serious problem in Korea because of its high incidence. The incidence of neonatal tetanus is not changed since past 10 years rather than decreased. Prevention is most important although therapeutic regimen advances recently. As Schofield et al.25 and Mac-Lennan et al.3) studied, active immunization of pregnant women with plain toxoids or AIPO4 toxoids... |
We have reported a case o£ 10 year old boy having a renal carbuncle which is very rare disease and reviewed literatures. Diagnosis has been established by clinical symptoms and signs, including irregular high fever and tender, egg-sized mass on the left costovertebral area, IVP and renal scanning. The patient was completely cured after drainage following incision and antibiotic therapy for... |
Pancreatitis is considered generally to be an unusual condition during infancy and childhood, but it may be more common in childhood than previously suspected. A case of acute pancreatitis in a 12-5/12 years-old boy is reported with related literatures. Comparative value of serum and urinary amylase was also studied to evaluate the clinical course in this case. |
Congenital choledochal cyst is a rarity throughout the world and its symptoms are variable and its diagnosis is not very easy. Several cases have been reported in Korea and they had more than two symptoms of the classic triad such as abdominal mass, jaundice and upper abdominal pain. A case of congenital choledochal cyst found in an 11 3/12 year... |
We have clinically observed 39 patients 'of abdominal tumors who were admitted in Severance-Hospital during the past 10 years from April 1960 to March 1970. Unfortunately follow-up study couldn’t be made. The following results were obtained. 1) Of total cases observed, 25 patients were male and 14 patients female. 2)The majority of the patients, 34 (87%) were under 6 years of age and... |