Purpose : The adverse reactions of prostaglandin E1(PGE1) are troublesome in the preoperative management of critical patients with ductus dependent congenital heart disease, and a preparation with less adverse reactions is preferable. The effects of Lipo PGE1, a new preparation of PGE1 contained in lipid microspheres, were compared with those of conventional PGE1(PGE1-CD). Methods : Lipo PGE1 was infused at a rate of 5... |
Double aortic arch is the most common type of symptomatic vascularring. In most patients, the symptoms are manifested at birth or in early infancy. Double aortic arch usually has more severe symptoms than other types of complete vascular rings. We experienced one case of complete duplicated double aortic arch with left descending aorta and left patent ductus arteriosus. A one-day-old female neonate was transferred... |
The clinical studies were performed on 304 patients with heart disease who had been received corrective heart surgery at Kosin Medical Center from July, 1984 to December, 1991. The results were follows : 1) Out of 304 patients, 162 cases (53.3%) were male and 142 cases (46.7%) were female and sex ratio was 1.15 : 1.35 cases (11.5%) had clinical cyanosis and... |
Congenital tricuspid stenosis is ancommon congenital heart anomaly. Tricuspid stenosis is usually associated with other anomalies, most commonly severe pulmonary stenosis or atresia with secondary hypoplasia of the right ventricle. Clinically it may be difficult to distinguish from tricuspid atresia. A case of congenital tricuspid stenosis in a 32 day-old-girl is presented. The patient had cyanosis and dyspnea. Echocardiographic study revealed... |
Cerebrocostomandibular Syndrome is characterized by micrognathia, cleft palate, multiple thorax deformity and frequently, mental deficiency. Respiratory compromise is a common cause of death. We experienced a case of cerebrocostomandibular syndrome with congeniyal heart disease in a 2 day old female baby with the chief complaint of cyanosis and respiratory difficulty since birth, She was delivered by cesarian section due to delayed... |
A clinical study was made on 533 patients with cardiovascular disease who were admitted to pediatric department of Chonbuk National University Hospital and performed cardiac catheterization and cineangiography from February 1984 to August 1991. The results were as follows; 1) The ratio of male to female was about 0.81:1; among 533 cases, male 283cases, male 283cases, female 295cases. 2)The age distribution of the... |
This is a 28-year analysis of 5,653 cases with congenital heart disease who underwent cardiac catheterization at Yonsei Medical Center from 1964 to 1991. Form 1964, there was a steady increment in the number of catheterized cases with CHD until the late 1970's when the patients population began to increase rapidlly. This was undoubtedly set off by the introduction of the... |
In patients with certain types of congenital heart malformations, an adequate interatrial communi- cation is essential for survival and balloon atrial septostomy (BAS) is a life saving procedure in these infants. However, BAS alone is not successful in older infants and children with thickened atrial septum, and blade septostomy is indicated in these situations. This procedure so far has not been reported in Korean literature... |
Balloon atrial septostomy is accepted as the best initial palliative treatment in infants with certain types of cyanotic congenital heart disease and the importance of prompt creation of atrial communi- cation can not be overemphasized in these patients. Balloon atrial septostomy is performed through femoral vein using percutaneous technique in most cases and is rarely done by cut down approach. However, percutaneous femoral vein... |
Cardiac catheterization, cineangiography and surgical analysis of 220 cases of congenital heart disease diagnosed by 2-D echocardiography was made, retrospectively from mar. 1985 to sep. 1989, who were admitted to the department of pediatrics Kosin Medical College Hospital. The results were analysed as follows; 1) 22 cases of 23 were correctly diagnosed in ASD, sensitivity and specificity of subxiphoid 2-D echocardiogram were 95.7% and 99.6% respectively. 2) 109... |
Children with cyanotic congenital heart disease (CCHD) and secondary polycythemia exhibit increased susceptibility to hemorrhage or thrombosis. The hemostatic disorder manifests itself by the occurrence of excessive hemorrhage after surgery, and by increased incidence of cerebrovascular accident of a thrombotic nature during life. To assess whether the severity of polycythemia in children with CCHD is correlated with coagula- tion abnormalities, hematologic studies with preoperative and... |
A retrospective study of 10 years* experience with surgical treatment of congenital heart disease in the St. Mary’s Hospital from 1978 to 1987 was made. Data were analyzed on 188 children with congenital heart disease who had received corrective heart surgery under the age of 18 years. The results were as follows: 1) Out of 188 patients, ventricular septal defect(54.2% of all) was the most... |
Thes is a study on changes of plasma renin activity (PRA) and aldosterone concentration (PAC) which was obtained before and after heart operation in 26 normotensive children with congenital heart diseases without renal disease admitted in Chungnam National University Hospital for cardiac catheterization with angiogram and heart operation from Apr. 1988 to Aug. 1988 to confirm any differences of PRA and PAC between groups... |
A variety of urinary tract anomalies were detected in 1,569 children with congenital heart disease during their cardiac evaluation with cardiac cineangiography in the Department of Pediatrics, Seoul National University Children’s Hospital within a period from October 1985 to April 1988. The incidence, nature and course of these urinary tract anomalies were analyzed and the results were as follows; 1) The number of male children... |
PRA’s in peripheral vein, both renal veins, and inferior vena cava (IVC) were measured in 25 normotensive children without renal disease undergoing cardiac catheterization for their underlying cyanotic congenital heart disease. And we presented the results as reference values/ranges of PRA in children. 1) There was no significant difference in PRA between both side renal veins at any absolute PRA levels with a mean ratio (RT/LT)... |
This study was designed to assess the accuracy of pulmonary (Qp) and systemic blood flow (Qs) and the ratio of pulmonary to systemic blood flow (Qp/Qs) measured by non-invasive range-gated pulsed Doppler echocardiography. Thirty five children with congenital heart disease, aged 4 months to 15 years, admitted for cardiac operation to this hospital, were studied. Cardiac outputs were measured by 2-dimensional range-gated pulsed Doppler... |
The association of congenital heart disease in patients with Down syndrome has been recognized for nearly 100 years. A wide variety of congenital heart diseases have been identified in these patients. This is the report of clinical evaluation of 105 patients with congenital heart disease in Down syndrome, experienced at the Seoul National University Hospital, during past 6 years from Jan. 1980... |
In 101 heart disease patients, the radionuclide angiocardiography(RNA) were performed.
Quantitation of left to right shunts were obtained by RNA and oximetry method in 41 patients simultaneously.
A comparison of the values for Qp/Qs ratio obtained by RNA & oximetry in those patients revealed a good correlation coefficient of 0.87(P |
The occurrence of congenital heart disease can be explained by genetic or environmental aspects. But these factors act separately only in about 10% and most of all, which reaches up to 90%, are inherited by the pattern of multifactorial inheritance, in which there is an underlying genetic predisition, usually produced by the small effects of many genes interacting with an... |
A heart disease screening program was performed on 15,685 primary school children in Seoul City from the first to sixth grade to estimate the prevalence of heart diseases. Among the 15,685 children examined, 45 were confirmed to have heart disease (2.9/1,000) Out of the 45 children, 38 had congenital heart disease(2.4/1,000) and 7 had rheumatic heart disease(0.4/1,000) and the ratio... |
To assess the validity of Echocardiographic criteria for pulmonary arterial hypertension we studied pulmonary valve motion in 75 congenital heart disease children. 75 patients were divided into two groups, A and B. The group A consisted of 39 patients who had normal pulmonary arterial pressure, group B consisted of 36 patients who had pulmonary arterial hypertension(pulmmonary artery mean pressure more... |
From July 1980 to June 1983, total 468 cases of infants of congenital heart disease were studied, who needed intensive care in infancy at Seoul National University Hospital. 1)Among 468 cases, 285 cases were diagnosed by cardiac catheterization or cardiac surgery and the other 183 cases by only clinical base. 2)Relative frequencies of these individual anomalies were in order of... |
Cor triatriatum is a rare congenital cardiac anomaly in which the left atrium is divided into two chambers by an abnormal fibro-muscular septum with, a small opening or not, product pulmonary venous obstruction and pulmonary hypertension. Three cases of cor triatriatum were observed at the Dept, of Pediatrics, Seoul National University. Each patient had no specific problem during early infancy, and presented... |
Cardiac arrhythmia which was observed during 5 years and 10 months from September 1975 to June 1981 on 11, 273 ECG records of the pediatric patients were analysed. Simple sinus arrhythmia and bundle branch blocks were excluded from this study. 602 cases of arrhythmia were seen among the 11,273 cases(5.3%). The types of arrhythmia in the order of frequency are:... |